Medulloepithelioma (diktyoma).

Medulloepithelioma (diktyoma) presenting as a perforated, infected eye.

A case of embryonal medulloepithelioma (diktyoma) presenting with perforated infected eye in a 13-year-old Black African girl is described. The tumour mass occupied most of the deformed eye, and invasion of the sclera anteriorly was seen. There was no evidence of orbital or distant tumour involvement. It is suggested that with increasing age these tumours are more likely to show frankly maligna...

Medullo-epithelioma (diktyoma) of the eye.

Medulloepithelioma involving the iris.

The case is described of a benign medulloepithelioma in a child which originally was apparently confined to the iris.

Pathology of a unique type of teratoid medulloepithelioma.

A unique teratoid medulloepithelioma showing a conspicuous vascular component with orbital involvement is described.

On the Classification and Grading of Medulloepithelioma of the Eye.

Medulloepithelioma is a rare congenital tumor of the ciliary body and iris. The current classification and grading of medulloepithelioma shows inconsistencies and does not reflect clinical behavior. This position paper discusses the backgrounds of the current classification and intends to initiate a discussion on an alternative classification and grading scheme.